Ichthyosis self care, ichthyosis management

Condition analysis:
"Harlequin ichthyosis is the most severe form of a rare autosomal recessive condition called Congenital Ichthyosis. In Harlequin ichthyosis, an extremely thick scale encases the entire fetus, with deep fissures in the scale developing after birth. Plaques, measuring up to 4 or 5 cm on a side, have a diamond-like configuration resembling the suit of a harlequin clown. Premature birth and early death can occur due to respiratory distress, dehydration, electrolyte imbalance, temperature instability, and bacterial infections. Children that survive eventually shed the thick, hard plates and develop scaling and redness of the skin. In the past, harlequin ichthyosis was fatal; however, intensive supportive care and the use of drugs has improved survival. Life expectancy is unknown. Survival to age 14 years has been reported."

Instructions:
Self-care: Although self-help measures won't cure ichthyosis, they may help improve the appearance and feel of damaged skin. These measures may be beneficial:

-- Take long soaking baths to soften the skin. Then use a roughly-textured sponge, such as a loofa sponge, to remove the thickened scales.

-- Choose mild soaps that have added oils and fats. Avoid deodorant and antibacterial soaps, which are especially harsh on dry skin.

-- After washing or bathing, gently pat or blot your skin dry with a towel so that some moisture remains on the skin.

-- Apply the moisturizer or lubricating cream while your skin is still wet or moist from bathing. Choose a moisturizer that contains urea or propylene glycol a€" chemicals that help keep your skin moist. Petroleum jelly is another good choice. Cover the treated areas with plastic wrap to keep the petroleum jelly from staining clothes and furniture.

-- Twice daily applications of an over-the-counter product that contains salicylic acid may help. Salicylic acid helps the skin shed its dead skin cells.

-- Use a portable home humidifier or one attached to your furnace to add moisture to the air inside your home.